Title:
A giant cranial aneurysmal bone cyst associated with fibrous dysplasia
Authors:
J. Skadzie*, K. Ole*, O. Zagólski*, M. Moskaa**, M. Sztuka**, P. Stre k*, W. Wierzchowski*** and J. Tomik* **Neurotraumatology and ***Pathomorphology, Collegium Medicum,
Institutions:
Departments of *Otorhinolaryngology, Jagiellonian University, Kraków, Poland
Keywords:
Tumour; cranial base; paranasal sinuses; orbit
Pages:
29 - 33
Abstract:
A giant cranial aneurysmal bone cyst associated with fibrous dysplasia. An aneurysmal bone cyst (ABC) is a rare, benign fibro-osseous lesion, considered a vascular phenomenon secondary to fibrous dysplasia or a giant-cell tumour, and occurs mainly in long bones and vertebrae. In this case report a 16-year-old male presented with massive epistaxis. He was admitted with a 3-year history of chronic rhinitis, headaches, right ocular pain and recurrent epistaxis. CT scans showed a predominantly cystic, expansive mass obstructing both nasal cavities, extending to all paranasal sinuses and both orbits, with evidence of anterior cranial fossa skull base destruction. The patient underwent a cranio- facial resection of the tumour performed with an external approach and an immediate reconstruction of the dural defect. Histology confirmed the lesion was anABC associated with fibrous dysplasia. The patients recovery was complete.A large facial aneurysmal bone cyst can damage the facial skeleton and skull base, and requires excision by a combined external approach.
Issue:
Vol. 4, 2008, 1st trimester


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A giant cranial aneurysmal bone cyst associated with fibrous dysplasia