Title:
Pneumosinus dilatans and orbital meningioma in neurofibromatosis type 2
Authors:
T. Vauterin*, I. Mombaerts**, M. Jorissen*, R. Sciot*** and E. Legius****
Institutions:
*Department of Oto-Rhino-Laryngology, Head and Neck Surgery, **Department of Ophthalmology, ***Department of Pathology, University Hospital KULeuven, Kapucijnenvoer 33, 3000 Leuven, Belgium; ****Center of Human Genetics University Hospital Gasthuisberg, KULeuven, Herestraat 49, 3000 Leuven, Belgium
Keywords:
Neurofibromatosis type 2; pneumosinus dilatans; meningioma; orbit
Pages:
89 - 92
Abstract:
Pneumosinus dilatans and orbital meningioma in neurofibromatosis type 2. We report on a 9-year-old boy with neurofibromatosis type 2 and a progressive proptosis of the left eye. Imaging studies revealed a pneumosinus dila- tans of the left ethmoidal and frontal sinuses and an adjacent left orbital mass. Incision biopsy of the orbital mass showed a meningiothelial meningioma. Orbital and intracranial meningiomas are frequently associated with pneumosinus dila- tans. This report illustrates the relationship of pneumosinus dilatans, intra-orbital meningioma and neurofibromatosis type 2.
Issue:
Vol. 1, 2005, 2nd trimester


Download:
Pneumosinus dilatans and orbital meningioma in neurofibromatosis type 2