A 6-year-old girl with an extranasopharyngeal angiofibroma of the ethmoid

Juvenile nasopharyngeal angiofibroma is a rare, highly vascular tumor that originates from the pterygopalatine fossa and occurs almost exclusively in adolescent boys. Localizations outside the nasopharynx are uncommon. In this case report, the case of a 6-year-old girl with an ethmoidal angiofibroma is presented. Because of the localization, this was classified as an extranasopharyngeal angiofibroma (ENA). ENA can present at all ages and in both sexes but similar to juvenile nasopharyngeal angiofibroma, male patients are more affected. Clinical presentation depends on the localization. Although clinical presentation, radiologic appearance, and epidemiology differs from that of a juvenile nasopharyngeal angiofibroma, the histologic findings are similar.